in CF the CFTR passage is blocked via a mutation and so it doesnt allow Cl- throu
IN YOUNGER YEARS it is essential to have good familial support to help begin treatment etc
airway clearance by nebuliser use via mucolytic therapy
good nutritional managment
-salt intake
-calories
-vitamins
Regular MDT clinics (multi-disciplinary clinics)
what is the definition of a CF exacerbation?
one or more if the following which leads to need of antibiotic treatment based on the presence of 2 or more of
change of sputum
inc cough
inc malaise
anorexia/weight loss
drop in Peak Flow Test of more than 10% of normal